Chiari Malformations 01

Topic: Pediatric

Created on Tuesday, February 5 2008 by jdmiles

Last modified on Tuesday, February 5 2008.

 
        A) Patients with a Chiari III malformation have a cerebellar encephalocele
 
        B) Patients with a Chiari II malformation have a cerebellar encephalocele
 
        C) Patients with a Chiari I malformation usually have a lumbar meningomyelocele
 
        D) Patients with a Chiari III malformation have downward displacement of the medulla and 4th ventricle
 
        E) Patients with a Chiari III malformation usually have a lumbar meningomyelocele
 

 

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This question was created on February 05, 2008 by jdmiles.
This question was last modified on February 05, 2008.

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

ANSWERS AND EXPLANATIONS

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A) Patients with a Chiari III malformation have a cerebellar encephalocele

This answer is correct.

There were 4 types of malformations described by Hans Chiari that we now refer to as Chiari malformations. Chiari I is a protrusion of part of the cerebellar tonsils through the foramen magnum. In Chiari II, there is a Chiari I plus downward displacement of the medulla and 4th ventricle. A Chiari III malformation is defined as cervical spina bifida with a cerebellar encephalocele. The Chiari IV malformation (a term now not often used) is probably unrelated, and is defined as hypoplasia of the cerebellum, and does not involve protrusion of the tonsils through the foramen magnum. Syringomyelia, syringobulbia, and hydrocephalus are often seen in each of the Chiari I, II and III malformations. Patients with a Chiari II malformation almost always have a lumbar meningomyelocele.  (See References)

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B) Patients with a Chiari II malformation have a cerebellar encephalocele

This answer is incorrect.

There were 4 types of malformations described by Hans Chiari that we now refer to as Chiari malformations. Chiari I is a protrusion of part of the cerebellar tonsils through the foramen magnum. In Chiari II, there is a Chiari I plus downward displacement of the medulla and 4th ventricle. A Chiari III malformation is defined as cervical spina bifida with a cerebellar encephalocele. The Chiari IV malformation (a term now not often used) is probably unrelated, and is defined as hypoplasia of the cerebellum, and does not involve protrusion of the tonsils through the foramen magnum. Syringomyelia, syringobulbia, and hydrocephalus are often seen in each of the Chiari I, II and III malformations. Patients with a Chiari II malformation almost always have a lumbar meningomyelocele.  (See References)

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C) Patients with a Chiari I malformation usually have a lumbar meningomyelocele

This answer is incorrect.

There were 4 types of malformations described by Hans Chiari that we now refer to as Chiari malformations. Chiari I is a protrusion of part of the cerebellar tonsils through the foramen magnum. In Chiari II, there is a Chiari I plus downward displacement of the medulla and 4th ventricle. A Chiari III malformation is defined as cervical spina bifida with a cerebellar encephalocele. The Chiari IV malformation (a term now not often used) is probably unrelated, and is defined as hypoplasia of the cerebellum, and does not involve protrusion of the tonsils through the foramen magnum. Syringomyelia, syringobulbia, and hydrocephalus are often seen in each of the Chiari I, II and III malformations. Patients with a Chiari II malformation almost always have a lumbar meningomyelocele.  (See References)

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D) Patients with a Chiari III malformation have downward displacement of the medulla and 4th ventricle

This answer is incorrect.

There were 4 types of malformations described by Hans Chiari that we now refer to as Chiari malformations. Chiari I is a protrusion of part of the cerebellar tonsils through the foramen magnum. In Chiari II, there is a Chiari I plus downward displacement of the medulla and 4th ventricle. A Chiari III malformation is defined as cervical spina bifida with a cerebellar encephalocele. The Chiari IV malformation (a term now not often used) is probably unrelated, and is defined as hypoplasia of the cerebellum, and does not involve protrusion of the tonsils through the foramen magnum. Syringomyelia, syringobulbia, and hydrocephalus are often seen in each of the Chiari I, II and III malformations. Patients with a Chiari II malformation almost always have a lumbar meningomyelocele.  (See References)

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---

E) Patients with a Chiari III malformation usually have a lumbar meningomyelocele

This answer is incorrect.

There were 4 types of malformations described by Hans Chiari that we now refer to as Chiari malformations. Chiari I is a protrusion of part of the cerebellar tonsils through the foramen magnum. In Chiari II, there is a Chiari I plus downward displacement of the medulla and 4th ventricle. A Chiari III malformation is defined as cervical spina bifida with a cerebellar encephalocele. The Chiari IV malformation (a term now not often used) is probably unrelated, and is defined as hypoplasia of the cerebellum, and does not involve protrusion of the tonsils through the foramen magnum. Syringomyelia, syringobulbia, and hydrocephalus are often seen in each of the Chiari I, II and III malformations. Patients with a Chiari II malformation almost always have a lumbar meningomyelocele.  (See References)

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References:

1. Sklar, E.M.L., Ruiz, A., Quencer, R.M., and Falcone, S.F. (2004). Structural neuroimaging. In Bradley, W.G., Daroff, R.B., Fenichel, G.M., and Jankovic, J. (Eds.). Neurology in Clinical Practice, Fourth Edition. Butterworth Heinemann, Philadelphia, pp. 521-597 (ISBN:0750674695).	Advertising:
2. Sarnat, H.B., and Flores-Sarnat, L. (2004). Developmental disorders of the nervous system. In Bradley, W.G., Daroff, R.B., Fenichel, G.M., and Jankovic, J. (Eds.). Neurology in Clinical Practice, Fourth Edition. Butterworth Heinemann, Philadelphia, pp. 1763-1789 (ISBN:0750674695).	Advertising:
3. Rosenbaum, R.B., and Ciaverella, D.P. (2004). Disorders of bones, joints, ligaments, and meninges. In Bradley, W.G., Daroff, R.B., Fenichel, G.M., and Jankovic, J. (Eds.). Neurology in Clinical Practice, Fourth Edition. Butterworth Heinemann, Philadelphia, pp. 2189-2222 (ISBN:0750674695).	Advertising:

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pediatric
Chiari Malformations 01
Question ID: 020508139
Question written by J. Douglas Miles, (C) 2006-2009, all rights reserved.
Created: 02/05/2008
Modified: 02/05/2008
Estimated Permutations: 109200