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Neurocutaneous 09

Topic: Pathology

Created on Monday, February 16 2009 by gliageek

Last modified on Monday, February 16 2009.


Courtesy of Dr. Mark Cohen
This infant was born with a large cutaneous pigmented lesion, and these grayish macules in his meninges. Which of the following malformations is most likely to also be found in his brain?

 
        A) Dandy-Walker malformation
 
        B) Agenesis of corpus callosum
 
        C) Leptomeningeal gliomatosis
 
        D) Angiomatosis
 
        E) Holoprosencephaly
 

 


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This question was created on February 16, 2009 by gliageek.
This question was last modified on February 16, 2009.

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

ANSWERS AND EXPLANATIONS




A) Dandy-Walker malformation

This answer is correct.


Most frequent developmental abnormality in patients with neurocutaneous melanosis  (See References)

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B) Agenesis of corpus callosum

This answer is incorrect.


Though a frequent accompaniment to a wide variety of genetic syndromes, not common in NCM  (See References)

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C) Leptomeningeal gliomatosis

This answer is incorrect.


Occasionally encountered in NF-1  (See References)

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D) Angiomatosis

This answer is incorrect.


Part of Sturge-Weber disease  (See References)

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E) Holoprosencephaly

This answer is incorrect.


Trisomy 13  (See References)

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References:

1. Love, S., Louis, D.N., and Ellison, D.W. (2008). Greenfield's Neuropathology, 8th Edition. Oxford University Press, USA (ISBN:0340906820)Advertising:
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pathology
Neurocutaneous 09
Question ID: 021609122
Question written by gliageek. (C) FrontalCortex.com 2006-2009, all rights reserved. Created: 02/16/2009
Modified: 02/16/2009
Estimated Permutations: 120

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