Neurocutaneous 06

Topic: Pathology

Created on Monday, February 16 2009 by gliageek

Last modified on Monday, February 16 2009.

 
        A) Von Hippel-Lindau disease
 
        B) Schwannomatosis
 
        C) Sturge-Weber disease
 
        D) Neurofibromatosis, type 2
 
        E) Neurofibromatosis, type 1
 

 

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This question was created on February 16, 2009 by gliageek.
This question was last modified on February 16, 2009.

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

 

ANSWERS AND EXPLANATIONS

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A) von Hippel-Lindau disease

This answer is incorrect.

Meningeal hemangioblastoma may be seen in vHLD  (See References)

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B) Schwannomatosis

This answer is incorrect.

Does not include meningioangiomatosis  (See References)

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C) Sturge-Weber disease

This answer is incorrect.

SWD shows meningeal angiomatosis with associated cortical calcification  (See References)

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D) Neurofibromatosis, type 2

This answer is correct.

For reasons which are not at all clear, meningioangiomatosis in NF2 is nearly always asymptomatic, even when multiple  (See References)

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E) Neurofibromatosis, type 1

This answer is incorrect.

Meningioangiomatosis is NOT part of NF1, although included as part of VRD in older literature (before molecular separation of NF1 and NF2)  (See References)

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References:

1. Love, S., Louis, D.N., and Ellison, D.W. (2008). Greenfield's Neuropathology, 8th Edition. Oxford University Press, USA (ISBN:0340906820)

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pathology
Neurocutaneous 06
Question ID: 021609113
Question written by gliageek. (C) FrontalCortex.com 2006-2009, all rights reserved. Created: 02/16/2009
Modified: 02/16/2009
Estimated Permutations: 120